- This is a rare congenital hypoplasia of lymph vessels that causes lymphedema of the legs and recurrent cholestasis in infancy.
- Mainly found in Norway.
- Lymphedema of the legs
- Recurrent cholestasis in infancy
- Insufficient bile secretion
- Underdeveloped lymph vessels
- Treatment of lymphedema; dietary consideration; low fat diet with fat soluble vitamin supplements; liver transplant.